Syndromic orbital border hypoplasia

Syndromic orbital border hypoplasia is a rare disorder observed in two families to date and characterized by agenesis of the orbital margin, varying defects of the lacrimal passages, hypoplasia of the palpebral skin and tarsal plates and atresia of the nasolacrimal duct.

Iris atrophy

Loss of iris tissue (atrophy)


Total: 2

                       


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PMID (PMCID)
19770716
 MIXED_SAMPLE Adult
Fixed dilated pupil (urrets-zavalia syndrome) after deep anterior lamellar keratoplasty.
Niknam S, Rajabi MT.
Cornea. 2009;28(10):1187-90.
Decreased BCVA and visual symptoms at night (glare and halo) are late sequelae.A fixed dilated pupil with iris atrophy (Urrets-Zavalia syndrome) is an uncommon postoperative complication that was originally described after penetrating keratoplasty for keratoconus.
11285448
 MIXED_SAMPLE Adult
[Urrets-Zavalia syndrome].
Bourcier T, Laplace O, Touzeau O, Moldovan SM, Borderie V, Laroche L.
J Fr Ophtalmol. 2001;24(3):303-8.
We report four cases of Urrets-Zavalia Syndrome (fixed dilated pupil with iris atrophy) observed after penetrating keratoplasty.