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Aggressive systemic mastocytosis

A severe and rare form of systemic mastocytosis (SM) characterized by considerable infiltration of mast cells in different tissues.

Anemia

A reduction in erythrocytes volume or hemoglobin concentration.

Total: 1

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PMID (PMCID)
8876560	MALE	Middle Aged
	The presence of membrane-bound stem cell factor on highly immature nonmetachromatic mast cells in the peripheral blood of a patient with aggressive systemic mastocytosis.
	Castells MC, Friend DS, Bunnell CA, Hu X, Kraus M, Osteen RT, Austen KF. J Allergy Clin Immunol. 1996;98(4):831-40.
	A 58-year-old man was first seen with aggressive systemic mastocytosis manifested by urticaria pigmentosa, hepatosplenomegaly, generalized bone lesions, anemia, thrombocytopenia, monoclonal gammopathy, and increased urine histamine levels.