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Aggressive systemic mastocytosis

A severe and rare form of systemic mastocytosis (SM) characterized by considerable infiltration of mast cells in different tissues.

Hepatomegaly

Abnormally increased size of the liver.

Total: 1

(per page)

PMID (PMCID)
25009756 (4069804)	OTHER
	An unusual case of aggressive systemic mastocytosis mimicking hepatic cirrhosis.
	Zhang XY, Zhang WH. Cancer Biol Med. 2014;11(2):134-8.
	Hepatic involvement in aggressive systemic mastocytosis (ASM) is relatively common, and the main clinical features of this disease include hepatomegaly, portal hypertension, ascites, and fibrosis.