Oligodontia

Oligodontia is a rare developmental dental anomaly in humans characterized by the absence of six or more teeth.

Micrognathia

Developmental hypoplasia of the mandible.


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PMID (PMCID)
12401987
 MIXED_SAMPLE Child
Dominant inheritance of cleft palate, microstomia and micrognathia--possible linkage to the fragile site at 16q22 (FRA16B).
McKenzie F, Turner A, Withers S, Dalzell P, McGlynn M, Kirk EP.
Clin Dysmorphol. 2002;11(4):237-41.
Of interest is a previously described family with autosomal dominant inheritance of U-shaped cleft palate, microstomia, micrognathia and oligodontia where all affected members were shown to have the fragile site at 16q22 in a proportion of their cells [Bettex et al.