Kaposi sarcoma

A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.



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Narrow down the case reports



Total: 403 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(55.1%)
30212041
[Kaposi's Sarcoma Herpesvirus-associated Inflammatory Cytokine Syndrome (KICS) Improved by Antiretroviral Therapy in an HIV-infected Patient].
Nishiki S, Yanagisawa N, Sasaki S, Sekiya R, Sekiya N, Suganuma A, Ajisawa A, Akifumi I.
Kansenshogaku Zasshi. 2016;90(4):512-7.
Hepatosplenomegaly Anemia Pleural effusion
Anti-Retroviral Agents HIV Infections Homo sapiens Inflammation Male Middle Aged
2
(52.6%)
7997131
[Kaposi's sarcoma in young adults without evidence of HIV infection].
Freuler CB, Durlach RA, Toblli JE, Cicco J, Casas J.
Medicina (B Aires). 1994;54(2):145-9.
Subcutaneous nodule Ascites Hemolytic anemia Fever
CD4 CD8A
Adult Fatal Outcome HIV Seronegativity Homo sapiens Kaposi Sarcoma Male Middle Aged Neoplasm Invasiveness Nephrotic Syndrome
3
(44.2%)
26511991
The challenging diagnosis of haemophagocytic lymphohistiocytosis in an HIV-infected patient.
Azevedo L, Gerivaz R, Simoes J, Germano I.
BMJ Case Rep. 2015;2015:.
Hepatosplenomegaly Pancytopenia Fever
Adult Anti-Retroviral Agents Antineoplastic Agents Differential Diagnosis Fever HIV Infections Homo sapiens Immunocompromised Host Kaposi Sarcoma Lymphohistiocytosis, Hemophagocytic Male Pancytopenia Penile Neoplasms
4
(43.8%)
19795003
(2752788)
Kaposi sarcoma herpes virus-associated hemophagocytic syndrome complicated by multicentric castleman disease and kaposi sarcoma in a HIV-negative immunocompetent patient: an autopsy case.
Kim B, Jeon YK, Kim CW.
J Korean Med Sci. 2009;24(5):970-4.
Thrombocytopenia Hemolytic anemia Fever Lymphadenopathy
Autopsy HIV Seronegativity Herpesviridae Infections Homo sapiens Immunocompetence Kaposi Sarcoma Lymphohistiocytosis, Hemophagocytic Magnetic Resonance Imaging Male Middle Aged Polymerase Chain Reaction
5
(40.5%)
30843320
Pediatric post-transplant hepatic kaposi sarcoma due to donor-derived human herpesvirus 8.
Ocwieja KE, Vargas SO, Elisofon SA, Shulman DS, Lee CK, Fawaz R, Collins N, Vakili K, Sharma TS.
Pediatr Transplant. 2019;23(3):e13384.
Biliary atresia Viremia Portal vein thrombosis
Biliary Atresia Disease Progression Females Homo sapiens Infant Kaposi Sarcoma Liver Magnetic Resonance Imaging Male Postoperative Complications Tissue Donors
6
(39.1%)
18030193
Multicentric Castleman's disease masquerading as HIV-related lymphoma.
Dayyani F, Pantanowitz L, Sandridge TG, Sullivan RJ, Dezube BJ.
Am J Med Sci. 2007;334(4):317-9.
Splenomegaly Lymphoproliferative disorder
Adult Differential Diagnosis Homo sapiens Kaposi Sarcoma Lymphoma, AIDS-Related Male
6
(39.1%)
1316718
Coincident Kaposi sarcoma and T-cell lymphoma in a patient with the Wiskott-Aldrich syndrome.
Meropol NJ, Hicks D, Brooks JJ, Siminovitch KA, Fishman NO, Kant JA, Bennett JS.
Am J Hematol. 1992;40(2):126-34.
Splenomegaly Thrombocytopenia
NEU1 SPN
Adult Biopsy Cytomegalovirus DNA, Viral Enzyme-Linked Immunosorbent Assay HIV Homo sapiens Kaposi Sarcoma Male Polymerase Chain Reaction Spleen T-Cell Lymphoma T-Lymphocyte Time Factors Wiskott-Aldrich Syndrome
8
(38.5%)
8038237
Kaposi's sarcoma in an HIV-negative CLL patient as the cause of thrombocytopenia.
Wijermans PW, van Groningen K, van Royen EA, Bruijn JA.
Ann Hematol. 1994;68(6):307-10.
Thrombocytopenia Leukemia Microangiopathic hemolytic anemia Kaposi's sarcoma
TNC
Antineoplastic Agents Biopsy Blood Platelets Chronic Lymphocytic Leukemia HIV Seronegativity Homo sapiens Kaposi Sarcoma Lymphocyte Subset Radionuclide Imaging Skin Technetium Compounds Thrombocytopenia
9
(38.0%)
25276327
(4178280)
Multicentric Castleman's Disease and Kaposi's Sarcoma in a HIV-Positive Patient on Highly Active Antiretroviral Therapy.
Ortega L, Cooper CJ, Otoukesh S, Mojtahedzadeh M, Didia CS, Torabi A, Nahleh Z.
Rare Tumors. 2014;6(3):5480.
Hepatomegaly Lymphoproliferative disorder
10
(37.8%)
19364316
Fatal acute purulent pericarditis in a patient with renal transplant: a case report.
Mohsin N, Budruddin M, Amitabh J, Ehab M, Abbas P.
Exp Clin Transplant. 2009;7(1):62-5.
Diabetes mellitus Thrombophlebitis Hepatitis
Acute Disease Anti-Bacterial Agents Cardiac Arrest Fatal Outcome Females Graft Rejection Homo sapiens Immunosuppressive Agents Kidney Transplantation Middle Aged Pericardiectomy Pericarditis Renal Dialysis Staphylococcus aureus Thrombophlebitis
        

Phenotype(s) retrieved from Orphanet

    Total: 26

HPO ID Term Frequency
HP:0005353 Recurrent herpes Obligate (100%)
HP:0001034 Hypermelanotic macule Very frequent (99-80%)
HP:0002814 Abnormality of the lower limb Very frequent (99-80%)
HP:0008069 Neoplasm of the skin Very frequent (99-80%)
HP:0012733 Macule Very frequent (99-80%)
HP:0000479 Abnormal retinal morphology Frequent (79-30%)
HP:0001028 Hemangioma Frequent (79-30%)
HP:0001298 Encephalopathy Frequent (79-30%)
HP:0001743 Abnormality of the spleen Frequent (79-30%)
HP:0002721 Immunodeficiency Frequent (79-30%)
HP:0005523 Lymphoproliferative disorder Frequent (79-30%)
HP:0008940 Generalized lymphadenopathy Frequent (79-30%)
HP:0011024 Abnormality of the gastrointestinal tract Frequent (79-30%)
HP:0200034 Papule Frequent (79-30%)
HP:0200036 Skin nodule Frequent (79-30%)
HP:0000988 Skin rash Occasional (29-5%)
HP:0001004 Lymphedema Occasional (29-5%)
HP:0001392 Abnormality of the liver Occasional (29-5%)
HP:0001824 Weight loss Occasional (29-5%)
HP:0001945 Fever Occasional (29-5%)
HP:0002014 Diarrhea Occasional (29-5%)
HP:0002088 Abnormal lung morphology Occasional (29-5%)
HP:0005293 Venous insufficiency Occasional (29-5%)
HP:0011793 Neoplasm by anatomical site Occasional (29-5%)
HP:0012378 Fatigue Occasional (29-5%)
HP:0200035 Skin plaque Occasional (29-5%)


Phenotype(s) retrieved from case reports

    Total: 95

HPO ID Term # of case reports
HP:0002721 Immunodeficiency 41
HP:0002664 Neoplasm 21
HP:0100742 Vascular neoplasm 11
HP:0005293 Venous insufficiency 8
HP:0032252 Granuloma 8
HP:0031690 Opportunistic infection 7
HP:0100026 Arteriovenous malformation 7
HP:0001028 Hemangioma 6
HP:0001370 Rheumatoid arthritis 6
HP:0002090 Pneumonia 6
HP:0002202 Pleural effusion 6
HP:0005306 Capillary hemangioma 6
HP:0030731 Carcinoma 6
HP:0100726 Kaposi's sarcoma 6
HP:0002861 Melanoma 5
HP:0002716 Lymphadenopathy 4
HP:0005523 Lymphoproliferative disorder 4
HP:0012115 Hepatitis 4
HP:0100242 Sarcoma 4
HP:0200034 Papule 4
HP:0001876 Pancytopenia 3
HP:0001909 Leukemia 3
HP:0002671 Basal cell carcinoma 3
HP:0004947 Arteriovenous fistula 3
HP:0010783 Erythema 3
HP:0000969 Edema 2
HP:0001048 Cavernous hemangioma 2
HP:0001945 Fever 2
HP:0002204 Pulmonary embolism 2
HP:0002781 Upper airway obstruction 2
HP:0002860 Squamous cell carcinoma 2
HP:0025615 Abscess 2
HP:0032163 Molluscum contagiosum 2
HP:0100827 Lymphocytosis 2
HP:0000083 Renal insufficiency 1
HP:0000099 Glomerulonephritis 1
HP:0000100 Nephrotic syndrome 1
HP:0000155 Oral ulcer 1
HP:0000166 Severe periodontitis 1
HP:0000230 Gingivitis 1
HP:0000389 Chronic otitis media 1
HP:0000704 Periodontitis 1
HP:0000952 Jaundice 1
HP:0001019 Erythroderma 1
HP:0001045 Vitiligo 1
HP:0001052 Nevus flammeus 1
HP:0001055 Erysipelas 1
HP:0001369 Arthritis 1
HP:0001482 Subcutaneous nodule 1
HP:0001513 Obesity 1
HP:0001541 Ascites 1
HP:0001698 Pericardial effusion 1
HP:0001824 Weight loss 1
HP:0001873 Thrombocytopenia 1
HP:0001937 Microangiopathic hemolytic anemia 1
HP:0002019 Constipation 1
HP:0002028 Chronic diarrhea 1
HP:0002094 Dyspnea 1
HP:0002099 Asthma 1
HP:0002619 Varicose veins 1
HP:0002835 Aspiration 1
HP:0002862 Bladder carcinoma 1
HP:0002878 Respiratory failure 1
HP:0003002 Breast carcinoma 1
HP:0003040 Arthropathy 1
HP:0003072 Hypercalcemia 1
HP:0003418 Back pain 1
HP:0005263 Gastritis 1
HP:0005425 Recurrent sinopulmonary infections 1
HP:0005550 Chronic lymphatic leukemia 1
HP:0007209 Facial paralysis 1
HP:0009710 Chilblains 1
HP:0010628 Facial palsy 1
HP:0011850 Parotitis 1
HP:0012089 Arteritis 1
HP:0012156 Hemophagocytosis 1
HP:0012203 Onychomycosis 1
HP:0012219 Erythema nodosum 1
HP:0012490 Panniculitis 1
HP:0012733 Macule 1
HP:0020071 Viremia 1
HP:0025127 Actinic keratosis 1
HP:0030350 Erythematous papule 1
HP:0030433 Osteoid osteoma 1
HP:0030880 Raynaud phenomenon 1
HP:0031492 Epithelial neoplasm 1
HP:0031864 Bacteremia 1
HP:0032282 Contact dermatitis 1
HP:0045073 Serositis 1
HP:0100279 Ulcerative colitis 1
HP:0100684 Salivary gland neoplasm 1
HP:0100749 Chest pain 1
HP:0100769 Synovitis 1
HP:0200043 Verrucae 1
HP:0200119 Acute hepatitis 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID