Rank (Similarity) |
PMID (PMCID) |
|
---|---|---|
4 (4.0%) |
10410549 |
[Severe adult-type Williams-Campbell syndrome (Williams-Campbell-type bronchiectasis)]. Kimoto T, Kawamura T, Nakahara Y, Mochizuki Y. Nihon Kokyuki Gakkai Zasshi. 1999;37(5):429-32. |
Dyspnea | ||
Bronchiectasis Fluoroscopy Homo sapiens Male Radiography, Thoracic Respiratory Insufficiency Syndrome X-Ray Computed Tomography | ||
4 (4.0%) |
9498979 |
Lung transplantation for Williams-Campbell syndrome. Palmer SM Jr, Layish DT, Kussin PS, Oury T, Davis RD, Tapson VF. Chest. 1998;113(2):534-7. |
Pneumonia | ||
Adult Airway Obstruction Bronchi Bronchial Diseases Bronchiectasis Cartilage Diseases Fatal Outcome Homo sapiens Ischemia Lung Transplantation Male Pneumonia, Bacterial Postoperative Complications Pseudomonas Infections Pseudomonas aeruginosa Pulmonary Emphysema Respiratory Insufficiency Syndrome | ||
4 (4.0%) |
9493457 |
[An adult case of Williams-Campbell syndrome associated with pulmonary hypertension and a severe decrease in ventilatory response]. Amano S, Yoshida Y, Shimizu H, Takeda T, Urabe N, Mizoo A, Kimura H, Kuriyama T. Nihon Kyobu Shikkan Gakkai Zasshi. 1997;35(11):1265-70. |
Hypertension | ||
Adult Bronchial Diseases Bronchiectasis Cartilage Diseases Homo sapiens Hypercapnia Hypoxia Male Pulmonary Hypertension Respiratory Insufficiency Syndrome | ||
4 (4.0%) |
8797568 |
Mortality following adenotonsillectomy in a patient with Williams-Campbell syndrome. Kirse DJ, Tryka AF, Seibert RW, Bower CM. Arch Otolaryngol Head Neck Surg. 1996;122(9):1007-10. |
Enlarged tonsils | ||
Adenoidectomy Ambulatory Surgical Procedures Bronchiectasis Child Fatal Outcome Homo sapiens Hypertrophy Male Palatine Tonsil Syndrome Tonsillectomy | ||
4 (4.0%) |
8265276 |
Familial congenital bronchiectasis: Williams-Campbell syndrome. Jones VF, Eid NS, Franco SM, Badgett JT, Buchino JJ. Pediatr Pulmonol. 1993;16(4):263-7. |
Bronchiectasis | ||
Bronchi Bronchiectasis Child, Preschool Females Homo sapiens Infant, Newborn Syndrome | ||
4 (4.0%) |
6296528 |
[Irreversible generalized pulmonary emphysema resulting from destructive bronchitis and bronchiolitis following adenovirus infection]. Manzke H. Klin Padiatr. 1982;194(6):387-92. |
Emphysema | ||
Adenovirus Infections Adenovirus Infections, Human Asthma Bronchiectasis Bronchiolitis, Viral Bronchitis Differential Diagnosis Homo sapiens Infant Male Pulmonary Emphysema Syndrome | ||
4 (4.0%) |
3597897 |
Congenital bronchiectasis due to cartilage deficiency: CT demonstration. Watanabe Y, Nishiyama Y, Kanayama H, Enomoto K, Kato K, Takeichi M. J Comput Assist Tomogr. 1987;11(4):701-3. |
Bronchiectasis | ||
Bronchi Bronchiectasis Females Homo sapiens Middle Aged Syndrome X-Ray Computed Tomography | ||
4 (4.0%) |
2232375 |
[Williams-Campbell syndrome complicated by multiple meniscus signs in an adult case; is it a characteristic finding?]. Fujishita M, Kataoka R, Kobayashi M, Miyoshi I. Nihon Kyobu Shikkan Gakkai Zasshi. 1990;28(7):1018-23. |
Pneumonia | ||
Bronchi Bronchiectasis Females Homo sapiens Middle Aged Syndrome | ||
4 (4.0%) |
1856896 |
Case report: computed tomography findings in Williams-Campbell syndrome. Kaneko K, Kudo S, Tashiro M, Kishikawa T, Nakanishi Y, Yamada H. J Thorac Imaging. 1991;6(2):11-3. |
Bronchiectasis | ||
Bronchiectasis Cyst Homo sapiens Male Middle Aged Pulmonary Emphysema Syndrome X-Ray Computed Tomography | ||
4 (4.0%) |
937831 |
Probable familial congenital bronchiectasis due to cartilage deficiency (Williams-Campbell syndrome). Wayne KS, Taussig LM. Am Rev Respir Dis. 1976;114(1):15-22. |
Bronchiectasis | ||
Bronchi Bronchiectasis Bronchoscopy Females Homo sapiens Lung Male Respiratory Function Tests |
Total: 0
HPO ID | Term | Frequency |
---|
Total: 8
HPO ID | Term | # of case reports |
---|---|---|
HP:0002110 | Bronchiectasis | 15 |
HP:0002878 | Respiratory failure | 4 |
HP:0002094 | Dyspnea | 2 |
HP:0002780 | Bronchomalacia | 2 |
HP:0000822 | Hypertension | 1 |
HP:0002097 | Emphysema | 1 |
HP:0002205 | Recurrent respiratory infections | 1 |
HP:0031245 | Productive cough | 1 |
Total: 0
Gene Symbol | Gene Name | Entrez Gene ID |
---|