Plasmacytoma

Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations.



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Total: 1002 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(43.2%)
25075597
Plasmacytoma presenting as missing rib on chest film: a case report and review of the literature.
Caffery T, Foy M.
J La State Med Soc. 2014;166(2):63-6.
Missing ribs
Adult Chest Homo sapiens Male Plasmacytoma Radiography, Thoracic
2
(42.7%)
29797838
Multiple myeloma presenting as mandibular pain.
Crowley M, Cronin O, Sleeman D, McKenna J.
J Ir Dent Assoc. 2016;62(5):276-278.
Mandibular pain
Biopsy Females Homo sapiens Mandible Mandibular Neoplasms Multiple Myeloma Pain
3
(42.2%)
30282157
[A case of extramedullary plasmacytoma of the nasal cavity].
Huo MX, Liu Z, Liu QX.
Lin Chung Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2018;32(15):1194-1195.
Nasal obstruction Chronic sinusitis
3
(42.2%)
17823407
Sinonasal plasmacytoma in a cat.
Schoniger S, Bridger N, Allenspach K, Mantis P, Rest J, Steeves E.
J Vet Diagn Invest. 2007;19(5):573-7.
Sinusitis Rhinitis
Animals Cat Diseases Felis catus Females Plasmacytoma
5
(40.9%)
29581951
(5863021)
Unusual malignant neoplasms occurring around dental implants: A report of 2 cases.
Oh SH, Kang JH, Seo YK, Lee SR, Choi YS, Hwang EH.
Imaging Sci Dent. 2018;48(1):59-65.
Sinusitis
5
(40.9%)
24847501
Multiple myeloma in bisphosphonate-affected jaws--a diagnostic challenge: case report.
Katkar RA, Katz J, Moreb JS, Nair MK.
Quintessence Int. 2014;45(7):613-7.
Sinusitis
Bisphosphonate-Associated Osteonecrosis of the Jaw Cone-Beam Computed Tomography Diphosphonates Homo sapiens Magnetic Resonance Imaging Male Middle Aged Multiple Myeloma
5
(40.9%)
14968081
[Orbital extension of sinus plasmacytoma secondarily transforming into multiple myeloma: a case study].
Balayre S, Gicquel JJ, Mercie M, Dighiero P.
J Fr Ophtalmol. 2004;27(1):67-71.
Chronic sinusitis
Adult Antineoplastic Agents Antineoplastic Agents, Hormonal Antineoplastic Agents, Phytogenic Antineoplastic Combined Chemotherapy Protocols Biopsy Diplopia Exophthalmos Homo sapiens Male Maxillary Sinus Maxillary Sinus Neoplasms Methylprednisolone Hemisuccinate Multiple Myeloma Orbital Neoplasms Paranasal Sinus Neoplasms Plasmacytoma Visual Acuity X-Ray Computed Tomography
5
(40.9%)
14571657
Solitary extramedullary plasmacytoma of the maxillary sinus. Case report.
Exarchakos G, Korantzopoulos P, Bai M, Xanthopoulos J, Tzouvara E, Skevas A.
Acta Otorhinolaryngol Belg. 2003;57(3):217-20.
Sinusitis
Females Homo sapiens Immunohistochemistry Maxillary Sinus Neoplasms Plasmacytoma Radiotherapy, High-Energy X-Ray Computed Tomography
5
(40.9%)
1854702
Solitary extramedullary plasmacytoma of the maxillary antrum and orbit presenting as acute bacterial orbital cellulitis.
Kelly SP, Lloyd IC, Anderson H, Joyce PW, Pace-Balzan A.
Br J Ophthalmol. 1991;75(7):438-9.
Sinusitis
Cellulitis Dysgerminoma Homo sapiens Male Maxillary Sinus Neoplasms Middle Aged Neoplasms, Multiple Primary Orbital Neoplasms Plasmacytoma Pneumococcal Infections Testicular Neoplasms
10
(39.0%)
16749751
Intraoperative magnetic resonance imaging-augmented transoral resection of axial disease.
Kaibara T, Hurlbert RJ, Sutherland GR.
Neurosurg Focus. 2001;10(2):E4.
Basilar invagination
C2
Aged, 80 and over Arnold Chiari Malformation Cervical Vertebrae Decompression, Surgical Homo sapiens Intraoperative Period Magnetic Resonance Imaging Middle Aged Plasmacytoma Spinal Neoplasms
        

Phenotype(s) retrieved from Orphanet

    Total: 0

HPO ID Term Frequency


Phenotype(s) retrieved from case reports

    Total: 179

HPO ID Term # of case reports
HP:0002664 Neoplasm 85
HP:0002835 Aspiration 38
HP:0030731 Carcinoma 32
HP:0001271 Polyneuropathy 18
HP:0005523 Lymphoproliferative disorder 15
HP:0032252 Granuloma 13
HP:0000952 Jaundice 12
HP:0002202 Pleural effusion 10
HP:0002861 Melanoma 9
HP:0031047 Paraproteinemia 9
HP:0001541 Ascites 8
HP:0002860 Squamous cell carcinoma 8
HP:0030150 Plasmacytosis 7
HP:0100242 Sarcoma 7
HP:0001909 Leukemia 6
HP:0002716 Lymphadenopathy 6
HP:0003072 Hypercalcemia 6
HP:0002094 Dyspnea 5
HP:0002176 Spinal cord compression 5
HP:0002576 Intussusception 5
HP:0009830 Peripheral neuropathy 5
HP:0025615 Abscess 5
HP:0100646 Thyroiditis 5
HP:0000520 Proptosis 4
HP:0000969 Edema 4
HP:0001028 Hemangioma 4
HP:0002090 Pneumonia 4
HP:0003002 Breast carcinoma 4
HP:0005202 Helicobacter pylori infection 4
HP:0012115 Hepatitis 4
HP:0012315 Histiocytoma 4
HP:0001085 Papilledema 3
HP:0001945 Fever 3
HP:0002015 Dysphagia 3
HP:0002027 Abdominal pain 3
HP:0002721 Immunodeficiency 3
HP:0010614 Fibroma 3
HP:0012735 Cough 3
HP:0100658 Cellulitis 3
HP:0100825 Cheilitis 3
HP:0000246 Sinusitis 2
HP:0000501 Glaucoma 2
HP:0000508 Ptosis 2
HP:0000620 Dacryocystitis 2
HP:0000651 Diplopia 2
HP:0000793 Membranoproliferative glomerulonephritis 2
HP:0000853 Goiter 2
HP:0000872 Hashimoto thyroiditis 2
HP:0001082 Cholecystitis 2
HP:0001138 Optic neuropathy 2
HP:0001289 Confusion 2
HP:0001433 Hepatosplenomegaly 2
HP:0001978 Extramedullary hematopoiesis 2
HP:0002196 Myelopathy 2
HP:0002385 Paraparesis 2
HP:0002756 Pathologic fracture 2
HP:0002862 Bladder carcinoma 2
HP:0002878 Respiratory failure 2
HP:0003003 Colon cancer 2
HP:0003418 Back pain 2
HP:0008462 Cervical instability 2
HP:0010550 Paraplegia 2
HP:0012125 Prostate cancer 2
HP:0012366 Basilar invagination 2
HP:0030156 Bence Jones Proteinuria 2
HP:0031281 Sialadenitis 2
HP:0031357 Glomeruloid hemangioma 2
HP:0031500 Abdominal mass 2
HP:0032404 Testicular mass 2
HP:0100727 Histiocytosis 2
HP:0100796 Orchitis 2
HP:0200036 Skin nodule 2
HP:0200123 Chronic hepatitis 2
HP:0000083 Renal insufficiency 1
HP:0000093 Proteinuria 1
HP:0000100 Nephrotic syndrome 1
HP:0000112 Nephropathy 1
HP:0000126 Hydronephrosis 1
HP:0000135 Hypogonadism 1
HP:0000212 Gingival overgrowth 1
HP:0000265 Mastoiditis 1
HP:0000572 Visual loss 1
HP:0000648 Optic atrophy 1
HP:0000771 Gynecomastia 1
HP:0000790 Hematuria 1
HP:0000819 Diabetes mellitus 1
HP:0000821 Hypothyroidism 1
HP:0000843 Hyperparathyroidism 1
HP:0000921 Missing ribs 1
HP:0000938 Osteopenia 1
HP:0000961 Cyanosis 1
HP:0000979 Purpura 1
HP:0001007 Hirsutism 1
HP:0001056 Milia 1
HP:0001067 Neurofibromas 1
HP:0001101 Iritis 1
HP:0001250 Seizures 1
HP:0001287 Meningitis 1
HP:0001332 Dystonia 1
HP:0001336 Myoclonus 1
HP:0001369 Arthritis 1
HP:0001370 Rheumatoid arthritis 1
HP:0001482 Subcutaneous nodule 1
HP:0001618 Dysphonia 1
HP:0001635 Congestive heart failure 1
HP:0001649 Tachycardia 1
HP:0001698 Pericardial effusion 1
HP:0001701 Pericarditis 1
HP:0001733 Pancreatitis 1
HP:0001735 Acute pancreatitis 1
HP:0001742 Nasal obstruction 1
HP:0001873 Thrombocytopenia 1
HP:0001875 Neutropenia 1
HP:0001880 Eosinophilia 1
HP:0001894 Thrombocytosis 1
HP:0001903 Anemia 1
HP:0001919 Acute kidney injury 1
HP:0001972 Macrocytic anemia 1
HP:0001974 Leukocytosis 1
HP:0002014 Diarrhea 1
HP:0002098 Respiratory distress 1
HP:0002099 Asthma 1
HP:0002102 Pleuritis 1
HP:0002105 Hemoptysis 1
HP:0002204 Pulmonary embolism 1
HP:0002240 Hepatomegaly 1
HP:0002249 Melena 1
HP:0002352 Leukoencephalopathy 1
HP:0002592 Gastric ulcer 1
HP:0002653 Bone pain 1
HP:0002754 Osteomyelitis 1
HP:0002781 Upper airway obstruction 1
HP:0002870 Obstructive sleep apnea 1
HP:0002955 Granulomatosis 1
HP:0002961 Dysgammaglobulinemia 1
HP:0003074 Hyperglycemia 1
HP:0003401 Paresthesia 1
HP:0003419 Low back pain 1
HP:0003470 Paralysis 1
HP:0004389 Intestinal pseudo-obstruction 1
HP:0005214 Intestinal obstruction 1
HP:0005263 Gastritis 1
HP:0005374 Cellular immunodeficiency 1
HP:0005550 Chronic lymphatic leukemia 1
HP:0005987 Multinodular goiter 1
HP:0007141 Sensorimotor neuropathy 1
HP:0008200 Primary hyperparathyroidism 1
HP:0010280 Stomatitis 1
HP:0010307 Stridor 1
HP:0010628 Facial palsy 1
HP:0011896 Subconjunctival hemorrhage 1
HP:0012032 Lipoma 1
HP:0012050 Anasarca 1
HP:0012057 Superficial spreading melanoma 1
HP:0012062 Bone cyst 1
HP:0012089 Arteritis 1
HP:0012384 Rhinitis 1
HP:0012587 Macroscopic hematuria 1
HP:0012636 Retinal vein occlusion 1
HP:0012740 Papilloma 1
HP:0020110 Bone fracture 1
HP:0025289 Cervical lymphadenopathy 1
HP:0025406 Asthenia 1
HP:0030169 Gastric varix 1
HP:0030358 Non-small cell lung carcinoma 1
HP:0030433 Osteoid osteoma 1
HP:0030838 Hip pain 1
HP:0031003 Polyneuritis 1
HP:0031207 Hepatic hemangioma 1
HP:0031501 Pelvic mass 1
HP:0032026 Anetoderma 1
HP:0032061 Hypereosinophilia 1
HP:0032282 Contact dermatitis 1
HP:0032408 Breast lump 1
HP:0040276 Adenocarcinoma of the colon 1
HP:0100518 Dysuria 1
HP:0100561 Spinal cord lesion 1
HP:0100750 Atelectasis 1
HP:0200034 Papule 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID