Rapidly progressive glomerulonephritis




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Narrow down the case reports



Total: 864 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(56.2%)
19301455
Antiglomerular basement membrane disease associated with Castleman disease.
Lv J, Zhang H, Zhou F, Zou W, Singh AK, Wang H.
Am J Med Sci. 2009;337(3):206-9.
Hematuria Splenomegaly Anemia
IL6
Adult Anti-Glomerular Basement Membrane Disease Follow-Up Studies Homo sapiens Male
2
(55.1%)
11793099
Glomerular involvement in myelodysplastic syndromes.
Bogdanovic R, Kuzmanovic M, Markovic-Lipkovski J, Ognjanovic M, Micic D, Stankovic I, Stajic N, Nikolic V, Bunjevacki G.
Pediatr Nephrol. 2001;16(12):1053-7.
Proteinuria Hepatosplenomegaly Anemia
Child Females Glucocorticoids Homo sapiens Infant Kidney Glomerulus Nephrotic Syndrome
3
(49.1%)
9708618
Infective endocarditis-induced crescentic glomerulonephritis dramatically improved by plasmapheresis.
Daimon S, Mizuno Y, Fujii S, Mukai K, Hanakawa H, Otsuki N, Yasuhara S, Saga T, Koni I.
Am J Kidney Dis. 1998;32(2):309-13.
Purpura Anemia Fever
Anti-Infective Agents Bacterial Endocarditis Differential Diagnosis Females Glomerulonephritis Homo sapiens Middle Aged Plasmapheresis Streptococcal Infections
4
(48.7%)
26120578
(4478318)
Antineutrophil Cytoplasmic Antibodies-Negative Pauci-Immune Crescentic Glomerulonephritis Associated with Multiple Myeloma.
Anaele CU, Srisung W, Tomacruz Y, Laski M.
Case Rep Nephrol Dial. 2015;5(2):124-9.
Normocytic anemia Acidosis Hepatitis
4
(48.7%)
10897595
[A case of hepatitis C virus-associated glomerulonephropathy presenting with MPO-ANCA-positive rapidly progressive glomerulonephritis].
Igaki N, Nakaji M, Moriguchi R, Akiyama H, Tamada F, Goto T.
Nihon Jinzo Gakkai Shi. 2000;42(4):353-8.
Proteinuria Anemia Hepatitis
Anti-Inflammatory Agents Antineutrophil Cytoplasmic Antibodies Disease Progression Females Glomerulonephritis Hepatitis C, Chronic Hepatitis C-Like Viruses Homo sapiens
6
(45.6%)
15478302
[Bone marrow aplasia during hemodialysis successfully treated with cyclosporine. Report of one case].
Vega J, Rodriguez Mde L, Vasquez A, Torres C.
Rev Med Chil. 2004;132(8):989-94.
Pancytopenia Hemolytic anemia Vitamin B12 deficiency
Adult Aplastic Anemia Homo sapiens IGA Glomerulonephritis Immunosuppressive Agents Kidney Transplantation Male Pancytopenia Renal Dialysis
7
(45.3%)
25753276
Bartonella henselae infection-associated vasculitis and crescentic glomerulonephritis leading to renal allograft loss.
Chaudhry AR, Chaudhry MR, Papadimitriou JC, Drachenberg CB.
Transpl Infect Dis. 2015;17(3):411-7.
Splenomegaly Fever Lymphoproliferative disorder
Bartonella henselae Cat-Scratch Disease Females Glomerulonephritis Homo sapiens Immunocompromised Host Kidney Transplantation Middle Aged Vasculitis
8
(44.2%)
12577674
[Corticoid-sensitive nephrotic syndrome in children with myelodysplastic syndromes].
Bogdanovic R, Kuzmanovic M, Markovic-Lipkovski J, Ognjanovic M, Micic D, Stankovic I, Stajic N, Nikolic V, Bunjevacki G.
Srp Arh Celok Lek. 2002;130(9-10):323-8.
Proteinuria Hepatosplenomegaly Pancytopenia
Child Child, Preschool Females Glucocorticoids Homo sapiens Nephrotic Syndrome Primary Myelofibrosis
9
(43.7%)
27801920
Hydralazine-Induced ANCA Vasculitis in the Setting of Acute Clostridium Difficile Infection.
Rasla S, El Meligy A, Cucu DF.
R I Med J (2013). 2016;99(11):41-43.
Proteinuria Anemia Vomiting
Adrenal Cortex Hormones Antihypertensive Agents Antineutrophil Cytoplasmic Antibodies Clostridium Infections Clostridium difficile Enterocolitis, Pseudomembranous Females Glomerulonephritis Hemorrhage Homo sapiens Kidney Vasculitis X-Ray Computed Tomography
9
(43.7%)
25933141
Mycophenolate-Induced Posterior Reversible Encephalopathy Syndrome.
Khajuria B, Khajuria M, Agrawal Y.
Am J Ther. 2016;23(4):e1072-3.
Edema Hemolytic anemia Bowel incontinence
Adult Females Glomerulonephritis Homo sapiens Immunosuppressive Agents Lupus Nephritis Posterior Leukoencephalopathy Syndrome Seizures Severity of Illness Index
        

Phenotype(s) retrieved from Orphanet

    Total: 0

HPO ID Term Frequency


Phenotype(s) retrieved from case reports

    Total: 132

HPO ID Term # of case reports
HP:0000099 Glomerulonephritis 56
HP:0040223 Pulmonary hemorrhage 37
HP:0000123 Nephritis 32
HP:0000112 Nephropathy 30
HP:0000100 Nephrotic syndrome 26
HP:0002955 Granulomatosis 24
HP:0001370 Rheumatoid arthritis 23
HP:0012578 Membranous nephropathy 20
HP:0000979 Purpura 18
HP:0100584 Endocarditis 18
HP:0000093 Proteinuria 17
HP:0002090 Pneumonia 15
HP:0000790 Hematuria 11
HP:0001945 Fever 11
HP:0032252 Granuloma 10
HP:0000083 Renal insufficiency 9
HP:0000793 Membranoproliferative glomerulonephritis 8
HP:0000822 Hypertension 8
HP:0006689 Bacterial endocarditis 8
HP:0012089 Arteritis 8
HP:0100820 Glomerulopathy 8
HP:0000096 Glomerulosclerosis 7
HP:0012593 Nephrotic range proteinuria 7
HP:0000819 Diabetes mellitus 6
HP:0001919 Acute kidney injury 6
HP:0012115 Hepatitis 6
HP:0030731 Carcinoma 6
HP:0002099 Asthma 5
HP:0000097 Focal segmental glomerulosclerosis 4
HP:0001970 Tubulointerstitial nephritis 4
HP:0002105 Hemoptysis 4
HP:0002907 Microscopic hematuria 4
HP:0100646 Thyroiditis 4
HP:0000246 Sinusitis 3
HP:0001903 Anemia 3
HP:0002027 Abdominal pain 3
HP:0002829 Arthralgia 3
HP:0002878 Respiratory failure 3
HP:0005575 Hemolytic-uremic syndrome 3
HP:0006515 Interstitial pneumonitis 3
HP:0008682 Acute tubular necrosis 3
HP:0100778 Cryoglobulinemia 3
HP:0000836 Hyperthyroidism 2
HP:0001271 Polyneuropathy 2
HP:0001733 Pancreatitis 2
HP:0001824 Weight loss 2
HP:0001894 Thrombocytosis 2
HP:0001909 Leukemia 2
HP:0001920 Renal artery stenosis 2
HP:0001937 Microangiopathic hemolytic anemia 2
HP:0002098 Respiratory distress 2
HP:0002113 Pulmonary infiltrates 2
HP:0002202 Pleural effusion 2
HP:0002206 Pulmonary fibrosis 2
HP:0002249 Melena 2
HP:0002583 Colitis 2
HP:0002721 Immunodeficiency 2
HP:0032326 Methicillin-resistant Staphylococcus aureus infection 2
HP:0100519 Anuria 2
HP:0000031 Epididymitis 1
HP:0000126 Hydronephrosis 1
HP:0000133 Gonadal dysgenesis 1
HP:0000388 Otitis media 1
HP:0000541 Retinal detachment 1
HP:0000969 Edema 1
HP:0000988 Skin rash 1
HP:0001025 Urticaria 1
HP:0001082 Cholecystitis 1
HP:0001269 Hemiparesis 1
HP:0001287 Meningitis 1
HP:0001298 Encephalopathy 1
HP:0001369 Arthritis 1
HP:0001658 Myocardial infarction 1
HP:0001659 Aortic regurgitation 1
HP:0001701 Pericarditis 1
HP:0001735 Acute pancreatitis 1
HP:0001744 Splenomegaly 1
HP:0001875 Neutropenia 1
HP:0001876 Pancytopenia 1
HP:0001878 Hemolytic anemia 1
HP:0001880 Eosinophilia 1
HP:0002013 Vomiting 1
HP:0002014 Diarrhea 1
HP:0002018 Nausea 1
HP:0002094 Dyspnea 1
HP:0002110 Bronchiectasis 1
HP:0002133 Status epilepticus 1
HP:0002170 Intracranial hemorrhage 1
HP:0002204 Pulmonary embolism 1
HP:0002239 Gastrointestinal hemorrhage 1
HP:0002321 Vertigo 1
HP:0002586 Peritonitis 1
HP:0002595 Ileus 1
HP:0002754 Osteomyelitis 1
HP:0002860 Squamous cell carcinoma 1
HP:0002905 Hyperphosphatemia 1
HP:0002960 Autoimmunity 1
HP:0003002 Breast carcinoma 1
HP:0005523 Lymphoproliferative disorder 1
HP:0008677 Congenital nephrotic syndrome 1
HP:0008757 Unilateral vocal cord paralysis 1
HP:0008940 Generalized lymphadenopathy 1
HP:0009830 Peripheral neuropathy 1
HP:0011109 Chronic sinusitis 1
HP:0011458 Abdominal symptom 1
HP:0011946 Bronchiolitis obliterans 1
HP:0012050 Anasarca 1
HP:0012213 Decreased glomerular filtration rate 1
HP:0012219 Erythema nodosum 1
HP:0012224 Circulating immune complexes 1
HP:0012234 Agranulocytosis 1
HP:0012378 Fatigue 1
HP:0012486 Myelitis 1
HP:0012579 Minimal change glomerulonephritis 1
HP:0012595 Mild proteinuria 1
HP:0012819 Myocarditis 1
HP:0025343 Lupus anticoagulant 1
HP:0025363 Endocapillary hypercellularity 1
HP:0025439 Pharyngitis 1
HP:0030157 Flank pain 1
HP:0030171 Perirenal hematoma 1
HP:0031035 Chronic infection 1
HP:0031273 Shock 1
HP:0031864 Bacteremia 1
HP:0032061 Hypereosinophilia 1
HP:0032118 Retinitis 1
HP:0100279 Ulcerative colitis 1
HP:0100614 Myositis 1
HP:0100699 Scarring 1
HP:0100735 Hypertensive crisis 1
HP:0100758 Gangrene 1
HP:0200123 Chronic hepatitis 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID