IgG4-related kidney disease

A rare renal disease occurring in the setting of a systemic IgG4 related disease. Renal manifestations include tubulointerstitial nephritis (TIN), membranous glomerulonephritis with or without TIN, IgA nephropathy, membranoproliferative glomerulonephritis, mesangioproliferative immune complex glomerulonephritis, sclerosing pyelitis, IgG4-related plasma cell arteritis, and hydronephrosis associated with IgG4 related retroperitoneal fibrosis or ureteral inflammatory pseudotumor. Patients present with acute or chronic renal failure and radiographic mass lesion.



患者の 徴候・症状 を入力


症例報告を絞り込む



合計: 28 （症例報告）

   


（表示件数）
対応する徴候・症状  遺伝子  変異  キーワード（MeSH）
順位
（類似度）		 PMID
(PMCID)
1
(36.8%)		 25849674
(4360725)
 Acute Interstitial Nephritis and Membranous Nephropathy in the Context of IgG4-Related Disease.
Stylianou K, Maragkaki E, Tzanakakis M, Stratakis S, Gakiopoulou H, Daphnis E.
Case Rep Nephrol Dial. 2015;5(1):44-8.
顔面麻痺 Sialadenitis
2
(27.8%)		 25838652
(4379619)
 Immunoglobulin G4-related tubulointerstitial nephritis associated with interstitial pulmonary disease: Report of a case with review of literature.
Saravanan M, Alexander S, Matthai SM, Korula A, Varughese S, Tamilarasi V.
Indian J Nephrol. 2015;25(2):113-6.
尿細管間質性腎炎 Sialadenitis
3
(4.0%)		 31192228
 IgG4-Related Kidney Disease: A Curious Case of Interstitial Nephritis with Hypocomplementemia.
Wong ETY, Lahiri M, Teh M, Leo CCH.
Case Rep Nephrol Dial. 2019;9(2):49-54.
腎炎
3
(4.0%)		 30651091
 Simultaneous occurrence of IgG4-related Tubulointerstitial nephritis and colon adenocarcinoma with hepatic metastasis: a case report and literature review.
Gou SJ, Xue LJ, Hu ZX.
BMC Nephrol. 2019;20(1):23.
尿細管間質性腎炎
ヒト 形質細胞 男 組織診 結腸癌 腎臓 腺癌 致死的転帰 間質性腎炎
3
(4.0%)		 30544121
 Immunoglobulin G4-Related Disease Arising from the Bladder Wall.
Kufukihara R, Niwa N, Mizuno R, Ohara K, Mikami S, Kikuchi E, Oya M.
Urol Int. 2018;:1-3.
前立腺炎
Immunoglobulin G4-Related Disease ヒト 男 膀胱疾患
3
(4.0%)		 30458736
(6245818)
 An IgA1-lambda-type monoclonal immunoglobulin deposition disease associated with membranous features in a patient with IgG4-related kidney disease: a case report.
Kitazawa A, Koda R, Yoshino A, Ueda Y, Takeda T.
BMC Nephrol. 2018;19(1):330.
蛋白尿
IGHA1
Immunoglobulin G4-Related Disease ヒト 男 間質性腎炎
3
(4.0%)		 30087220
 Immunoglobulin G4-related Kidney Disease Associated With Autoimmune Hemolytic Anemia.
Gou SJ, Yu SB, Qiu HY, Hu ZX.
Iran J Kidney Dis. 2018;12(4):243-246.
貧血
ヒト 免疫組織化学 副腎皮質ステロイド 生物学的マーカー 男 組織診 腎疾患 腎臓 自己免疫疾患
3
(4.0%)		 29709946
(6207830)
 A Refractory Case of Secondary Membranous Nephropathy Concurrent with IgG4-related Tubulointerstitial Nephritis.
Arai H, Toda N, Kamimatsuse R, Nishioka K, Endo S, Akiyama S, Maruyama S, Matsubara T, Yokoi H, Yanagita M.
Intern Med. 2018;57(19):2873-2877.
蛋白尿
Immunoglobulin G4-Related Disease ネフローゼ症候群 ヒト 中年 免疫抑制薬 抗炎症薬 男 膵炎 蛋白尿 間質性腎炎
3
(4.0%)		 28912998
(5585603)
 IgG4-Related Kidney Disease: Report of a Case Presenting as a Renal Mass.
Bianchi D, Topazio L, Gaziev G, Iacovelli V, Bove P, Mauriello A, Finazzi Agro E.
Case Rep Surg. 2017;2017:9690218.
微量アルブミン尿
3
(4.0%)		 28552902
(5459220)
 IgG4-Related Disease Manifesting as Interstitial Nephritis Accompanied by Hypophysitis.
Matsuda K, Saito A, Takeuchi Y, Fukami H, Sato H, Nagasawa T.
Am J Case Rep. 2017;18:593-598.
多尿
80歳以上 ヒト 尿崩症 男 自己免疫性下垂体炎 間質性腎炎
        

徴候・症状リスト（Orphanetデータベースから取得）

    合計: 0

HPO ID 徴候・症状 頻度


徴候・症状リスト（症例報告から取得）

    合計: 11

HPO ID 徴候・症状 症例報告数
HP:0001970 尿細管間質性腎炎 5
HP:0000123 腎炎 4
HP:0000024 前立腺炎 2
HP:0000099 糸球体腎炎 2
HP:0012578 膜性腎症 2
HP:0000083 腎不全 1
HP:0000793 膜性増殖性糸球体腎炎 1
HP:0001919 急性腎外傷 1
HP:0005576 尿細管間質 線維症 1
HP:0030151 胆管炎 1
HP:0030731 Carcinoma 1


疾患原因遺伝子リスト（Orphanetデータベースから取得）

    合計: 0

Gene Symbol 遺伝子名 Entrez Gene ID